Ectopic ureterocele without ureteral and calyceal dilatation (ureterocele disproportion): findings on urography and sonography

Department of Radiology, Children's Hospital, Boston, MA 02115.

Eight infants and children (six girls) were seen over a 13-year period with duplex collecting systems and ectopic ureteroceles. In each, there was striking dissimilarity in size between the large ureterocele and its diminutive ureter and calyces. The upper moiety did not function and, except for the ureterocele, the indirect urographic and direct sonographic signs of duplication were absent or subtle. We call this entity ureterocele disproportion. Seven patients presented with urinary infection and one was found to have hydronephrosis of a dilated lower moiety in utero. Five had ipsilateral lower-pole reflux, which ranged in degree from 3 to 5 (on a scale of 1-5). Two had bilateral duplication; one of these had a typical contralateral ectopic ureterocele. The diagnosis of ureterocele disproportion was strongly suggested by urography and sonography and was confirmed at cystoscopy by direct puncture of the ureterocele and opacification of the upper moiety. All had surgery. The approach varied and depended on the status of the lower moiety and the contralateral kidney. One had incision of the ureterocele only. Five with lower-pole reflux had excision of the ureterocele and ipsilateral common-sheath reimplantation.
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