AJR ARRS Member Benefits
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
QUICK SEARCH:   [advanced]


     

This Article
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Alert me to new issues of the journal
Right arrow Download to citation manager
Right arrow reprints & permissions
Citing Articles
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by STEINBACH, H. L.
Right arrow Articles by YOUNG, D. A.
Right arrow Search for Related Content
PubMed
Right arrow Articles by STEINBACH, H. L.
Right arrow Articles by YOUNG, D. A.
Social Bookmarking
Add to CiteULike   Add to Complore   Add to Connotea   Add to Del.icio.us   Add to Digg   Add to Reddit   Add to Technorati  
What's this?
American Journal of Roentgenology, Vol 97, 49-66, Copyright © 1966 by American Roentgen Ray Society

THE ROENTGEN APPEARANCE OF PSEUDOHYOP-PARATHYROIDISM (PH) AND PSEUDO-PSEUDO-HYPOPARATHYROIDISM (PPH)

DIFFERENTIATION FROM OTHER SYNDROMES ASSOCIATED WITH SHORT METACARPALS, METATARSALS, AND PHALANGES

HOWARD L. STEINBACH M.D.1 and DUANE A. YOUNG 1

1 From the Department of Radiology, University of California School of Medicine, San Francisco, California

Pseudohypoparathyroidism (PH) is a hereditary congenital abnormality consisting of 3 separate components: (1) metabolic abnormalities of low serum calcium and high phosphorus which do not respond adequately to parathyroid hormone; (2) short stature and disproportionate shortening of some metacarpals, metatarsals, and phalanges, which may develop after birth; (3) ossification or calcification of the soft tissues. The soft tissue ossification or calcification may be the initial lesion with skeletal deformity and characteristic electrolyte disturbance developing later.

Pseudo-pseudohypoparathyroidism (PPH) is a partial manifestation of the same syndrome with normal calcium and phosphorus levels in the serum.

The skeletal and soft tissue lessions have been tabulated and are presented. Similar lesions of the metacarpals, metatarsals and phalanges occur with multiple familial exostoses, Turner's syndrome, and other less common syndromes, but these have other roentgen, clinical, and genetic findings that indicate the correct diagnosis.


Add to CiteULike CiteULike   Add to Complore Complore   Add to Connotea Connotea   Add to Del.icio.us Del.icio.us   Add to Digg Digg   Add to Reddit Reddit   Add to Technorati Technorati    What's this?




HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
Copyright © 1966 by the American Roentgen Ray Society.