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Fig. 7B —24-year-old man with Loeys-Dietz syndrome and complicated
cardiovascular history. He underwent repair of aortic root at age of 8 years
and developed aortic arch dissection at age 17 years. Subsequent imaging
revealed 5-cm thoracoabdominal aortic aneurysm with chronic dissection, and
patient's entire descending and abdominal aortas were replaced with Dacron
(polyethylene terephthalate fiber, DuPont) graft. The patient developed
pancreatitis due to large aneurysm of superior mesenteric artery (Figs.
11A,
11B, and
11C). In the next month, he
was found to have 2.8-cm left internal carotid artery aneurysm, repaired with
graft. Additional aneurysms have been identified in innominate, bilateral
subclavian, vertebral, common carotid, internal thoracic, and common iliac
(Figs. 11A,
11B, and
11C) arteries. Thrombosed
right subclavian pseudoaneurysm (black arrows) with metallic density,
probably representing coils, is shown on coronal oblique volume rendering.
Vascular tortuosity of aorta and great vessels (white arrows) was
also identified. Noncardiovascular findings of Loeys-Dietz syndrome included
hypertelorism, bifid uvula, and musculoskeletal abnormalities.
